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Despite the controversy, this manuscript intends to clarify the mechanism of action of TMAO in AS and attempt to suit the degree of doubt

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Contrariamente a lo que sucede con los trastornos dependientes de vitaminas, en este caso la administracin de carnitina acta como destoxificante y lejos de interferir, aumenta la excrecin neonatal de derivados de acilcarnitinas, lo cual favorece el diagnstico posnatal

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